Cystic Fibrosis: Patient Care, Treatment, and Management Analysis

This report delves into the comprehensive management of Cystic Fibrosis, beginning with patient presentation, including symptoms like difficulty breathing and coughing, alongside relevant lab and diagnostic findings. The report outlines the assessment data, such as vital signs and observed conditions, and identifies the patient's primary reason for seeking healthcare and any pre-existing conditions. It then details expected outcomes, potential risk factors, and the nursing interventions implemented, such as patient education about the disease, medication, and self-management techniques like deep breathing exercises. Furthermore, the report highlights the genetic basis of Cystic Fibrosis, specifically the CFTR gene mutations, which lead to varying classes of the disease, and also covers dietary considerations to support lung and muscle health. This assignment provides a thorough exploration of the multifaceted aspects of patient care for individuals with Cystic Fibrosis.

Reason for Seeking Health Care
 Difficulty in breathing
 Pertinent coughing with pain in chest
Presenting Symptoms
 Patient reports difficulty in breathing and frequent coughing
 Patient diagnosed with cystic fibrosis
 Patient reports not having a good feeling
Lab and Diagnostics
BP: 115/76, Pulse Rate: 85, RR: 28, Temp. 101.8 ̊ F, SPO2: 88%,
Body weight: 30 kg
Assessment Data
 Patient experiences
difficulty in breathing
 Patient seems anxious
 Patient experiences pain
while coughing
 Patient seems to have an
infection within the
respiratory tract
 The patient is seen to
cough with rhonchi
Preexisting Conditions
 Cystic Fibrosis
Expected Outcomes
 The patient’s respiratory effort seems labored
 Ineffective airway clearance and mucous buildup within
the lungs
 Potential lung infection
Risk Factors
 Genetic mutation within the
CFTR gene could lead to
Classes I,II and III classic
CFTR. Whereas mutations
leading to Classes IV and V
are not so server
 Decline in lung function
 Consumption of balanced
meal to avoid damage to
pulmonary and muscle
tissues
Patient Education
 Providing patient and
family education about
cystic Fibrosis
 The patient would be
educated about
appropriate medication
with proper rationale
 The patient would be
educated about self-
management strategies
such as deep breathing
exercises to improve
breathing
Nursing Interventions
 Monitor the ability of the patient to clear mucous
secretions
 Administer mild breathing exercises to ease
breathing
 Referral to a psychotherapist for alleviating mood
and affect
 Devising an appropriate diet plan according to the
cultural and religious belief of the patient