Assignment On Nursing Care Plan.

Nursing Care Plan
CYSTIC FIBROSIS

CYSTIC FIBROSIS
Cystic fibrosis is an inherited disease mainly affecting the lungs and the
digestive system. In this case, the body secretes a thick and sticky mucus
which blocks the smooth airflow in the lungs and also obstructs the
pancreas
Symptoms
The clinical manifestations of cystic fibrosis in an individual are:
• Shortness of breath
• Coughing and wheezing
• No weight gain in spite of proper appetite
• Salty taste of the skin
Risk factors
• Genetics – since it is an inherited disorder it can run in families
• Lung disease
• Poor antibiotic treatment
• Mutation(CFTR)
• Race/Ethnicity – it is more common among the white peoples of Northern
Europe
Complexities
• Diabetes
• Chronic Respiratory failure
• Bowel problems
• Renal failure
• Nasal polyps
[Image Source: Verywellhealth.com,
2020]

Pathophysiology of Cystic Fibrosis
• The CFTR gene loses its function as a chloride ion
transporter owing to protein misfolding(Bergeron
and Cantin, 2019)
• As a result, abnormal transport of sodium and
chloride ions takes place across the cell membrane,
leading to ion imbalance
• This leads to the secretion of a thick, sticky and
slimy fluid in the lungs and the pancreas
• The airway in the lungs is blocked, which restricts
the normal and smooth airway circulation, resulting
in air trapping and other respiratory
problems(Cutting, Engelhardt and Zeitlin, 2019)
• The slimy and sticky fluid can also lead to infection
in the lungs and pancreas, since it cannot be
removed by cilia and helps in the trapping of
pathogenic bacteria such as Pseudomonas sp. and
Staphylococcus sp. resulting in chronic infection
[Image source:
Rc.rcjournal.com, 2020]